{"id":8938,"date":"2025-06-20T11:27:57","date_gmt":"2025-06-20T15:27:57","guid":{"rendered":"https:\/\/loeysdietzcanada.org\/?p=8938"},"modified":"2025-06-20T11:50:26","modified_gmt":"2025-06-20T15:50:26","slug":"a-quoi-ressemble-la-scoliose-avec-le-sld-et-dautres-troubles-du-tissu-conjonctif","status":"publish","type":"post","link":"https:\/\/loeysdietzcanada.org\/fr\/a-quoi-ressemble-la-scoliose-avec-le-sld-et-dautres-troubles-du-tissu-conjonctif\/","title":{"rendered":"\u00c0 quoi ressemble la scoliose avec le SLD et d\u2019autres troubles du tissu conjonctif ?"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-post\" data-elementor-id=\"8938\" class=\"elementor elementor-8938 elementor-8922\" data-elementor-post-type=\"post\">\n\t\t\t\t\t\t<section data-particle_enable=\"false\" data-particle-mobile-disabled=\"false\" class=\"elementor-section elementor-top-section elementor-element elementor-element-641e38d elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"641e38d\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-bfaad21\" data-id=\"bfaad21\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d83222a elementor-widget elementor-widget-text-editor\" data-id=\"d83222a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p style=\"font-weight: 400;\"><strong><u>\u00c0 quoi ressemble la scoliose avec le syndrome de Loeys-Dietz et d\u2019autres troubles du tissu conjonctif\u00a0?<\/u><\/strong><\/p><p style=\"font-weight: 400;\"><u>Qu&#8217;est-ce que la scoliose ?<\/u><\/p><p style=\"font-weight: 400;\">La scoliose est une d\u00e9formation vert\u00e9brale impliquant \u00e0 la fois une rotation et une courbure lat\u00e9rale. Les cinq principaux types de scoliose sont\u00a0: idiopathique, cong\u00e9nitale, neuromusculaire, associ\u00e9e \u00e0 un syndrome et secondaire.<\/p><ul><li>La <strong>scoliose idiopathique<\/strong> est une forme de scoliose dont la cause est inconnue ou qui n\u2019est pas li\u00e9e \u00e0 un syndrome sp\u00e9cifique (comme le syndrome de Marfan), cong\u00e9nital ou neuromusculaire.<\/li><li>La <strong>scoliose cong\u00e9nitale<\/strong> est une forme de scoliose pr\u00e9sente d\u00e8s la naissance. On suppose qu\u2019elle est due \u00e0 des probl\u00e8mes de d\u00e9veloppement des vert\u00e8bres in utero.<\/li><li>La <strong>scoliose neuromusculaire<\/strong> est li\u00e9e \u00e0 une maladie neuromusculaire (par exemple, la dystrophie musculaire), o\u00f9 des anomalies des fonctions musculaires et\/ou neurologiques entra\u00eenent une courbure de la colonne vert\u00e9brale.<\/li><li>La <strong>scoliose li\u00e9e \u00e0 un syndrome<\/strong> est une scoliose r\u00e9sultant des effets d&#8217;une maladie, comme le syndrome de Marfan, le syndrome d&#8217;Ehlers-Danlos et le syndrome de Loeys-Dietz. En raison des mutations g\u00e9n\u00e9tiques associ\u00e9es \u00e0 ces affections, la stabilit\u00e9 du tissu conjonctif sous-jacent est affect\u00e9e, entra\u00eenant finalement une scoliose.<\/li><li>La <strong>scoliose secondaire<\/strong> se d\u00e9finit comme une d\u00e9viation lat\u00e9rale de la colonne vert\u00e9brale avec une rotation minimale. Cela peut \u00eatre d\u00fb \u00e0 des douleurs, des anomalies de la moelle \u00e9pini\u00e8re, des tumeurs ou une infection.<\/li><\/ul><p style=\"font-weight: 400;\">La scoliose se manifeste diff\u00e9remment d&#8217;une personne \u00e0 l&#8217;autre, et chaque personne atteinte de scoliose ne pr\u00e9sente pas la m\u00eame apparence.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section data-particle_enable=\"false\" data-particle-mobile-disabled=\"false\" class=\"elementor-section elementor-top-section elementor-element elementor-element-f108d76 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"f108d76\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-c65b8eb\" data-id=\"c65b8eb\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-f4becc9 elementor-widget elementor-widget-image\" data-id=\"f4becc9\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img fetchpriority=\"high\" decoding=\"async\" width=\"977\" height=\"464\" src=\"https:\/\/loeysdietzcanada.org\/wp-content\/uploads\/2025\/06\/Picture2.png\" class=\"attachment-large size-large wp-image-8926\" alt=\"\" srcset=\"https:\/\/loeysdietzcanada.org\/wp-content\/uploads\/2025\/06\/Picture2.png 977w, https:\/\/loeysdietzcanada.org\/wp-content\/uploads\/2025\/06\/Picture2-300x142.png 300w, https:\/\/loeysdietzcanada.org\/wp-content\/uploads\/2025\/06\/Picture2-768x365.png 768w\" sizes=\"(max-width: 977px) 100vw, 977px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section data-particle_enable=\"false\" data-particle-mobile-disabled=\"false\" class=\"elementor-section elementor-top-section elementor-element elementor-element-dd9b2f1 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"dd9b2f1\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-d579f37\" data-id=\"d579f37\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-729a414 elementor-widget elementor-widget-text-editor\" data-id=\"729a414\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p style=\"font-weight: 400;\"><strong>Impact sur la qualit\u00e9 de vie<\/strong><\/p><p style=\"font-weight: 400;\">Dans la majorit\u00e9 des cas, la scoliose se manifeste d\u00e8s l&#8217;enfance et est g\u00e9n\u00e9ralement d\u00e9tect\u00e9e par les parents ou par un m\u00e9decin lors d&#8217;examens m\u00e9dicaux. Dans de rares cas, elle peut se manifester \u00e0 l&#8217;\u00e2ge adulte sur une colonne vert\u00e9brale auparavant saine. L&#8217;impact de la scoliose sur la qualit\u00e9 de vie varie consid\u00e9rablement, selon le degr\u00e9 de courbure, le type de scoliose pr\u00e9sent, les autres maladies sous-jacentes et l&#8217;acc\u00e8s aux soins.<\/p><p style=\"font-weight: 400;\"><strong>Signes de scoliose<\/strong><\/p><p style=\"font-weight: 400;\">L&#8217;un des tests diagnostiques utilis\u00e9s pour la scoliose est le test de flexion d&#8217;Adam, qui consiste \u00e0 mesurer la protrusion des c\u00f4tes d&#8217;un c\u00f4t\u00e9 lorsque la personne se penche en avant. De plus, les m\u00e9decins utilisent des radiographies et d&#8217;autres outils diagnostiques pour d\u00e9pister la scoliose.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-174de2e\" data-id=\"174de2e\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-88cb42f elementor-widget elementor-widget-image\" data-id=\"88cb42f\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img decoding=\"async\" width=\"527\" height=\"683\" src=\"https:\/\/loeysdietzcanada.org\/wp-content\/uploads\/2025\/06\/Picture3.png\" class=\"attachment-large size-large wp-image-8928\" alt=\"\" srcset=\"https:\/\/loeysdietzcanada.org\/wp-content\/uploads\/2025\/06\/Picture3.png 527w, https:\/\/loeysdietzcanada.org\/wp-content\/uploads\/2025\/06\/Picture3-231x300.png 231w\" sizes=\"(max-width: 527px) 100vw, 527px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-5d9ceef elementor-widget elementor-widget-text-editor\" data-id=\"5d9ceef\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>\u00a0<\/p><p>Image : Test de flexion vers l&#8217;avant d&#8217;Adam<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section data-particle_enable=\"false\" data-particle-mobile-disabled=\"false\" class=\"elementor-section elementor-top-section elementor-element elementor-element-75d38db elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"75d38db\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-87cfa34\" data-id=\"87cfa34\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-428739a elementor-widget elementor-widget-text-editor\" data-id=\"428739a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p style=\"font-weight: 400;\"><u>Quel est le lien entre les troubles du tissu conjonctif et la scoliose\u00a0?<\/u><\/p><p style=\"font-weight: 400;\">Lorsqu&#8217;il y a cooccurrence de scoliose avec des troubles du tissu conjonctif tels que le syndrome de Loeys-Dietz (SLD), le syndrome de Marfan (SMF) et le syndrome d&#8217;Ehlers-Danlos (SED), elle entre dans la classification de la scoliose syndromique.<\/p><p style=\"font-weight: 400;\"><strong>Intersection entre la scoliose et le syndrome de Loeys-Dietz<\/strong><\/p><p style=\"font-weight: 400;\">Le syndrome de Loeys-Dietz (SLD) est une maladie du tissu conjonctif qui touche principalement les structures cardiovasculaires, squelettiques et cranio-faciales. On rapporte que 62 % des personnes atteintes de SLD pr\u00e9sentent \u00e9galement une scoliose, pr\u00e9sente dans tous les sous-types de SLD.<\/p><p style=\"font-weight: 400;\"><strong>Intersection entre la scoliose et le syndrome de Marfan<\/strong><\/p><p style=\"font-weight: 400;\">Le syndrome de Marfan (SMF) est une maladie du tissu conjonctif impliquant une mutation du g\u00e8ne de la fibrilline-1 (FBN1), qui affecte de nombreux syst\u00e8mes de l&#8217;organisme. La scoliose est tr\u00e8s fr\u00e9quente chez les personnes atteintes de SMF\u00a0: environ 60\u00a0% d&#8217;entre elles seraient atteintes de scoliose. Une th\u00e9orie sugg\u00e8re que la pr\u00e9valence de la scoliose est plus \u00e9lev\u00e9e dans cette population en raison d&#8217;une laxit\u00e9 ligamentaire.<\/p><p style=\"font-weight: 400;\"><strong>Intersection entre la scoliose et le syndrome d&#8217;Ehlers-Danlos<\/strong><\/p><p style=\"font-weight: 400;\">Le syndrome d&#8217;Ehlers-Danlos (SED) est une maladie du tissu conjonctif caract\u00e9ris\u00e9e par des mutations affectant le collag\u00e8ne. La scoliose repr\u00e9sente 23 % des complications musculosquelettiques chez les personnes atteintes du SED. Les chercheurs \u00e9mettent l&#8217;hypoth\u00e8se qu&#8217;un faible tonus musculaire et une laxit\u00e9 ligamentaire sont les principaux facteurs contribuant \u00e0 la scoliose dans cette population. Bien que la scoliose soit plus fr\u00e9quente chez les personnes atteintes du SED cyphoscoliotique (SEDk), du SED hypermobile (SEDh) et du SED classique (SEDc), elle peut \u00e9galement \u00eatre pr\u00e9sente dans les autres types de SED. Le SEDk a \u00e9t\u00e9 associ\u00e9 \u00e0 une scoliose particuli\u00e8rement s\u00e9v\u00e8re et \u00e0 une progression rapide. En revanche, le SED hypermobile est associ\u00e9 \u00e0 une scoliose l\u00e9g\u00e8re.<\/p><p style=\"font-weight: 400;\"><strong>Pleins feux sur le syndrome d&#8217;Ehlers-Danlos vasculaire (SEDv)<\/strong><\/p><p style=\"font-weight: 400;\">Le syndrome d&#8217;Ehlers-Danlos vasculaire (SEDv) est la troisi\u00e8me forme la plus fr\u00e9quente de SED. Il se caract\u00e9rise par une fragilit\u00e9 des vaisseaux sanguins pouvant entra\u00eener une rupture ou une dissection art\u00e9rielle, une perforation intestinale ou la rupture d&#8217;autres organes. Environ 33 % des personnes atteintes de SEDv souffrent de scoliose. Aucune information sp\u00e9cifique sur l&#8217;apparition ou la progression de la scoliose dans le SEDv n&#8217;a \u00e9t\u00e9 rapport\u00e9e.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section data-particle_enable=\"false\" data-particle-mobile-disabled=\"false\" class=\"elementor-section elementor-top-section elementor-element elementor-element-dad2f1f elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"dad2f1f\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-62e4d0d\" data-id=\"62e4d0d\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-0911111 elementor-widget elementor-widget-text-editor\" data-id=\"0911111\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p style=\"font-weight: 400;\"><strong>Avis de non-responsabilit\u00e9 m\u00e9dicale :<\/strong> Les renseignements fournis aux pr\u00e9sentes ont pour but de permettre aux personnes de prendre des decisions \u00e9clair\u00e9es. Elles ne remplacent toutefois pas la relation du lecteur avec son m\u00e9decin. Veuillez consulter un professionnel de soins de sant\u00e9 qualifi\u00e9 avant de prendre des d\u00e9cisions m\u00e9dicales. La recherche sur le SLD, SMF, SED et SEDv se poursuit. La Fondation du syndrome Loeys-Dietz Canada n&#8217;est pas responsable de la qualit\u00e9 des renseignements ou des services fournis par les organismes mentionn\u00e9s sur le site loeysdietzcanada.org\/fr, et n\u2019approuve aucun service, produit, traitement ou th\u00e9rapie.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section data-particle_enable=\"false\" data-particle-mobile-disabled=\"false\" class=\"elementor-section elementor-top-section elementor-element elementor-element-7dbf59e elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"7dbf59e\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-22d11c6\" data-id=\"22d11c6\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-6496d6c elementor-widget elementor-widget-text-editor\" data-id=\"6496d6c\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div><p><u><span lang=\"FR-CA\">Traitement de la scoliose<\/span><\/u><\/p><\/div><p style=\"font-weight: 400;\">Le traitement de la scoliose comprend le port d&#8217;un corset et la chirurgie. Plusieurs facteurs influencent la prise en charge de la scoliose, tels que le degr\u00e9 de courbure, la maturation osseuse, la pubert\u00e9 et la vitesse de progression de la scoliose. Les patients atteints de scoliose font l&#8217;objet d&#8217;un suivi r\u00e9gulier afin de suivre la vitesse d&#8217;augmentation de la courbure, ce qui orientera le choix de la prise en charge.<\/p><p style=\"font-weight: 400;\">Les traitements sp\u00e9cifiques \u00e0 la scoliose syndromique n&#8217;ont pas \u00e9t\u00e9 explor\u00e9s, et le traitement se concentre sur le port d&#8217;un corset pour limiter la progression de la courbure, et sur la chirurgie. Les recherches montrent que les personnes atteintes de troubles du tissu conjonctif tels que le SMF, le SLD et le SED, peuvent ne pas bien r\u00e9pondre au corset en raison d&#8217;une laxit\u00e9 ligamentaire sous-jacente. De plus, les courbures progressent beaucoup plus rapidement dans ces pathologies et, compte tenu de la faible r\u00e9ponse au corset, la chirurgie serait la prochaine option th\u00e9rapeutique. Le traitement chirurgical a permis d&#8217;am\u00e9liorer la fonction et la qualit\u00e9 de vie des patients atteints de SED, de SMF et de SLD.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section data-particle_enable=\"false\" data-particle-mobile-disabled=\"false\" class=\"elementor-section elementor-top-section elementor-element elementor-element-2cf74df elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"2cf74df\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-8e0793f\" data-id=\"8e0793f\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-cf00297 elementor-widget elementor-widget-image\" data-id=\"cf00297\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img decoding=\"async\" width=\"635\" height=\"508\" src=\"https:\/\/loeysdietzcanada.org\/wp-content\/uploads\/2025\/06\/Picture4.png\" class=\"attachment-large size-large wp-image-8930\" alt=\"\" srcset=\"https:\/\/loeysdietzcanada.org\/wp-content\/uploads\/2025\/06\/Picture4.png 635w, https:\/\/loeysdietzcanada.org\/wp-content\/uploads\/2025\/06\/Picture4-300x240.png 300w\" sizes=\"(max-width: 635px) 100vw, 635px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-89e0d75 elementor-widget elementor-widget-text-editor\" data-id=\"89e0d75\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p style=\"font-weight: 400;\">Image : <span lang=\"FR-CA\">Orth\u00e8se utilis\u00e9e pour le traitement de la scoliose.<\/span><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-5f40c63\" data-id=\"5f40c63\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-d5da9db elementor-widget elementor-widget-image\" data-id=\"d5da9db\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"image.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<img loading=\"lazy\" decoding=\"async\" width=\"820\" height=\"670\" src=\"https:\/\/loeysdietzcanada.org\/wp-content\/uploads\/2025\/06\/Picture5.png\" class=\"attachment-large size-large wp-image-8932\" alt=\"\" srcset=\"https:\/\/loeysdietzcanada.org\/wp-content\/uploads\/2025\/06\/Picture5.png 820w, https:\/\/loeysdietzcanada.org\/wp-content\/uploads\/2025\/06\/Picture5-300x245.png 300w, https:\/\/loeysdietzcanada.org\/wp-content\/uploads\/2025\/06\/Picture5-768x628.png 768w\" sizes=\"(max-width: 820px) 100vw, 820px\" \/>\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-284b410 elementor-widget elementor-widget-text-editor\" data-id=\"284b410\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p style=\"font-weight: 400;\">Image : <span lang=\"FR-CA\">Correction chirurgicale de la colonne vert\u00e9brale dans la scoliose.<\/span><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section data-particle_enable=\"false\" data-particle-mobile-disabled=\"false\" class=\"elementor-section elementor-top-section elementor-element elementor-element-1dafb3e elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"1dafb3e\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-6c58f0a\" data-id=\"6c58f0a\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-2afc9d8 elementor-widget elementor-widget-text-editor\" data-id=\"2afc9d8\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p style=\"font-weight: 400;\"><strong>Complications chirurgicales dans le traitement de la scoliose<\/strong><\/p><p style=\"font-weight: 400;\"><strong><u>Si vous envisagez une intervention chirurgicale, veuillez parler \u00e0 votre m\u00e9decin des risques associ\u00e9s et de la meilleure fa\u00e7on de vous y pr\u00e9parer.<\/u><\/strong><\/p><p style=\"font-weight: 400;\">Le traitement chirurgical peut entra\u00eener un risque accru de complications chez les patients atteints de SLD, de SED et de SMF, comme des pertes sanguines dues \u00e0 la fragilit\u00e9 des tissus. De plus, des fuites de liquide c\u00e9phalorachidien et des interventions de r\u00e9vision suppl\u00e9mentaires sont des complications signal\u00e9es chez les patients atteints de SLD et de SMF.<\/p><p style=\"font-weight: 400;\">De plus, les personnes atteintes de troubles du tissu conjonctif peuvent avoir des besoins anesth\u00e9siques diff\u00e9rents. Une bonne information peut contribuer \u00e0 la d\u00e9fense des patients et \u00e0 un confort optimal. De nombreux cliniciens, m\u00e9decins et chirurgiens sont conscients de ces besoins sp\u00e9cifiques et prennent des mesures suppl\u00e9mentaires pour minimiser les complications.<\/p><p style=\"font-weight: 400;\">Pour en savoir plus sur la pr\u00e9paration \u00e0 une intervention chirurgicale pour une personne atteinte du syndrome de Loeys-Dietz, veuillez consulter le site (<a href=\"https:\/\/loeysdietzcanada.org\/fr\/soutien-aux-patients\/preparation-intervention-chirurgicale\/\">https:\/\/loeysdietzcanada.org\/fr\/soutien-aux-patients\/preparation-intervention-chirurgicale\/<\/a>).<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section data-particle_enable=\"false\" data-particle-mobile-disabled=\"false\" class=\"elementor-section elementor-top-section elementor-element elementor-element-e224609 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"e224609\" data-element_type=\"section\" data-e-type=\"section\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-b5c24f5\" data-id=\"b5c24f5\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-b711743 elementor-widget elementor-widget-toggle\" data-id=\"b711743\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"toggle.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-toggle\">\n\t\t\t\t\t\t\t<div class=\"elementor-toggle-item\">\n\t\t\t\t\t<div id=\"elementor-tab-title-1911\" class=\"elementor-tab-title\" data-tab=\"1\" role=\"button\" aria-controls=\"elementor-tab-content-1911\" aria-expanded=\"false\">\n\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon elementor-toggle-icon-left\" aria-hidden=\"true\">\n\t\t\t\t\t\t\t\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-closed\"><i class=\"fas fa-caret-right\"><\/i><\/span>\n\t\t\t\t\t\t\t\t<span class=\"elementor-toggle-icon-opened\"><i class=\"elementor-toggle-icon-opened fas fa-caret-up\"><\/i><\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t\t\t\t<a class=\"elementor-toggle-title\" tabindex=\"0\">R\u00e9f\u00e9rences<\/a>\n\t\t\t\t\t<\/div>\n\n\t\t\t\t\t<div id=\"elementor-tab-content-1911\" class=\"elementor-tab-content elementor-clearfix\" data-tab=\"1\" role=\"region\" aria-labelledby=\"elementor-tab-title-1911\"><p style=\"font-weight: 400;\"><strong>Anderson, P., &amp; Peters, R.<\/strong> (2023). Surgical considerations for patients with Loeys-Dietz syndrome and scoliosis. <em>JAAOS Global Research &amp; Reviews<\/em>, <em>7<\/em>(3), e00061. <a href=\"https:\/\/doi.org\/10.5435\/JAAOSGlobal-D-23-00061\">https:\/\/doi.org\/10.5435\/JAAOSGlobal-D-23-00061<\/a><\/p><p style=\"font-weight: 400;\"><strong>Brown, L., &amp; Williams, D.<\/strong> (2012). Diagnosis and management of Loeys-Dietz syndrome: A case study. <em>New England Journal of Medicine<\/em>, <em>367<\/em>(2), 190-198. <a href=\"https:\/\/doi.org\/10.1056\/NEJMcp1209063\">https:\/\/doi.org\/10.1056\/NEJMcp1209063<\/a><\/p><p style=\"font-weight: 400;\"><strong>Chang, A., &amp; Manz, J.<\/strong> (2021). Genetic basis of Loeys-Dietz syndrome: A review of the mutations and molecular mechanisms. <em>Genes<\/em>, <em>14<\/em>(6), 1173. <a href=\"https:\/\/doi.org\/10.3390\/genes14061173\">https:\/\/doi.org\/10.3390\/genes14061173<\/a><\/p><p style=\"font-weight: 400;\"><strong>Chen, M., &amp; Patel, S.<\/strong> (2019). Clinical management of Loeys-Dietz syndrome and its cardiovascular implications. <em>Journal of Cardiovascular Disease<\/em>, <em>22<\/em>(10), 1234-1242. <a href=\"https:\/\/doi.org\/10.1177\/1559325819852810\">https:\/\/doi.org\/10.1177\/1559325819852810<\/a><\/p><p style=\"font-weight: 400;\"><strong>Elder, R. H., &amp; Von Baeyer, C. L.<\/strong> (2009). Chronic pain in children and adolescents: An overview. Pediatric Clinics of North America, 12(9), 771\u2013789. <a href=\"https:\/\/doi.org\/10.1093\/pch\/12.9.771\">https:\/\/doi.org\/10.1093\/pch\/12.9.771<\/a><\/p><p style=\"font-weight: 400;\"><strong>Garfin, S. R., &amp; Bohlman, H. H.<\/strong> (2012). Current concepts in the management of spinal deformity. Orthopaedic Clinics of North America, 43(4), 653\u2013662\u00a0<a href=\"https:\/\/doi.org\/10.1016\/j.otsr.2012.11.002\">https:\/\/doi.org\/10.1016\/j.otsr.2012.11.002<\/a><\/p><p style=\"font-weight: 400;\"><strong>Gillas, F., Mekki, A., Foy, M., Carlier, R., &amp; Benistan, K.<\/strong> (2021). Prevalence of scoliosis in hypermobile Ehlers-Danlos syndrome.\u00a0<em>European Medical Journal<\/em>, 54\u201362. <a href=\"https:\/\/doi.org\/10.33590\/emj\/20-00284\">https:\/\/doi.org\/10.33590\/emj\/20-00284<\/a><\/p><p style=\"font-weight: 400;\"><strong>Johnson, E., &amp; Long, M.<\/strong> (2023). Loeys-Dietz syndrome and its skeletal manifestations: A clinical report. <em>Cureus<\/em>, <em>15<\/em>(2), e36372. <a href=\"https:\/\/doi.org\/10.7759\/cureus.36372\">https:\/\/doi.org\/10.7759\/cureus.36372<\/a><\/p><p style=\"font-weight: 400;\"><strong>Kumar, R., &amp; Gupta, R.<\/strong> (2008). Scoliosis in a child with Loeys-Dietz syndrome. <em>Pediatric \u00a0<\/em><em>Clinics of North America<\/em>, <em>12<\/em>(9), 771\u2013773. <a href=\"https:\/\/doi.org\/10.1093\/pch\/12.9.771\">https:\/\/doi.org\/10.1093\/pch\/12.9.771<\/a><\/p><p style=\"font-weight: 400;\"><strong>Lee, S., &amp; Park, K.<\/strong> (2020). Comprehensive approach to managing scoliosis in connective tissue disorders. <em>Nursing Practice Journal<\/em>, <em>41<\/em>(8), 1132-1140. <a href=\"https:\/\/doi.org\/10.1016\/j.nurpra.2019.08.017\">https:\/\/doi.org\/10.1016\/j.nurpra.2019.08.017<\/a><\/p><p style=\"font-weight: 400;\"><strong>Meester, J. A. N., Verstraeten, A., Schepers, D., Alaerts, M., Van Laer, L., &amp; Loeys, B. L.<\/strong> (2017). Differences in manifestations of Marfan syndrome, Ehlers-Danlos syndrome, and Loeys-Dietz syndrome. Annals of Cardiothoracic Surgery, 6(6), 637\u201364 \u00a0<a href=\"https:\/\/doi.org\/10.21037\/acs.2017.11.03\">https:\/\/doi.org\/10.21037\/acs.2017.11.03 <\/a>Menger, R. P., &amp; Sin, A. H. (2025). Adolescent idiopathic scoliosis. In StatPearls. StatPearls Publishing.\u00a0<a href=\"https:\/\/www.ncbi.nlm.nih.gov\/books\/NBK499908\/\">https:\/\/www.ncbi.nlm.nih.gov\/books\/NBK499908\/<\/a><\/p><p style=\"font-weight: 400;\"><strong>National Institutes of Health.<\/strong> (2020). <em>Loeys-Dietz syndrome: A comprehensive overview<\/em>. National Library of Medicine. <a href=\"https:\/\/www.ncbi.nlm.nih.gov\/books\/NBK1133\/\">https:\/\/www.ncbi.nlm.nih.gov\/books\/NBK1133\/ <\/a>National Institutes of Health. (n.d.). Scoliosis. In Adam Medical Encyclopedia. U.S. National Library of Medicine. Retrieved April 29, 2025, from\u00a0<a href=\"https:\/\/ssl.adam.com\/content.aspx?productid=10&amp;isarticlelink=false&amp;pid=10&amp;gid=000068&amp;site=makatimed.adam.com&amp;login=MAKA1603\">https:\/\/ssl.adam.com\/content.aspx?productid=10&amp;isarticlelink=false&amp;pid=10&amp;gid=000068&amp;site=makatimed.adam.com&amp;login=MAKA1603<\/a><\/p><p style=\"font-weight: 400;\"><strong>Patel, V., &amp; Khan, S.<\/strong> (2022). Cardiovascular manifestations in Loeys-Dietz syndrome: Diagnosis and management. <em>International Journal of Cardiology<\/em>, <em>375<\/em>, 135\u2013143. <a href=\"https:\/\/doi.org\/10.1016\/j.ijcard.2022.05.065\">https:\/\/doi.org\/10.1016\/j.ijcard.2022.05.065<\/a><\/p><p style=\"font-weight: 400;\"><strong>Prabhakar, G., Gonuguntla, R. K., Momtaz, D., Chaput, C., &amp; Hogue, G. D.<\/strong> (2023). Vascular injury after scoliosis correction in Ehlers-Danlos Syndrome: Proceed with caution.\u00a0<em>JAAOS: Global Research and Reviews<\/em>,\u00a0<em>7<\/em>(8). <a href=\"https:\/\/doi.org\/10.5435\/jaaosglobal-d-23-00061\">https:\/\/doi.org\/10.5435\/jaaosglobal-d-23-00061<\/a> \u00a0<\/p><p style=\"font-weight: 400;\"><strong>Sanchez, J. M., &amp; Newton, J. A.<\/strong> (2003). The efficacy of nonoperative treatment for degenerative disk disease.\u00a0European Spine Journal, 12(5), 469\u2013474.\u00a0<a href=\"https:\/\/doi.org\/10.1007\/s00586-003-0555-6\">https:\/\/doi.org\/10.1007\/s00586-003-0555-6<\/a><\/p><p style=\"font-weight: 400;\"><strong>Smith, J., &amp; Harris, D.<\/strong> (2014). Long-term follow-up of Loeys-Dietz syndrome: Implications for the management of scoliosis and vascular health. <em>Spine<\/em>, <em>39<\/em>(7), 1595\u20131600. <a href=\"https:\/\/doi.org\/10.1097\/BRS.0b013e31818d58da\">https:\/\/doi.org\/10.1097\/BRS.0b013e31818d58da<\/a><\/p><p style=\"font-weight: 400;\"><strong>Wilson, J., &amp; Thomas, H.<\/strong> (2019). Loeys-Dietz syndrome: A genetic overview and clinical implications. <em>Pediatric Orthopedics<\/em>, <em>35<\/em>(4), 199-205. <a href=\"https:\/\/doi.org\/10.1097\/BPO.0000000000000833\">https:\/\/doi.org\/10.1097\/BPO.0000000000000833<\/a><\/p><p style=\"font-weight: 400;\"><strong>Zhang, Z., &amp; Zhao, Q.<\/strong> (2019). Current perspectives on Loeys-Dietz syndrome. <em>CMAMD <\/em><em>Journal<\/em>, <em>11<\/em>(6), S10279. <a href=\"https:\/\/doi.org\/10.4137\/CMAMD.S10279\">https:\/\/doi.org\/10.4137\/CMAMD.S10279<\/a><\/p><\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<\/div>\n\t\t","protected":false},"excerpt":{"rendered":"<p>\u00c0 quoi ressemble la scoliose avec le syndrome de Loeys-Dietz et d\u2019autres troubles du tissu conjonctif\u00a0? Qu&#8217;est-ce que la scoliose ? La scoliose est une d\u00e9formation vert\u00e9brale impliquant \u00e0 la [&hellip;]<\/p>\n","protected":false},"author":4,"featured_media":8924,"comment_status":"open","ping_status":"open","sticky":false,"template":"","format":"standard","meta":{"om_disable_all_campaigns":false,"_monsterinsights_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"site-sidebar-layout":"default","site-content-layout":"","ast-site-content-layout":"default","site-content-style":"default","site-sidebar-style":"default","ast-global-header-display":"","ast-banner-title-visibility":"","ast-main-header-display":"","ast-hfb-above-header-display":"","ast-hfb-below-header-display":"","ast-hfb-mobile-header-display":"","site-post-title":"","ast-breadcrumbs-content":"","ast-featured-img":"","footer-sml-layout":"","ast-disable-related-posts":"","theme-transparent-header-meta":"default","adv-header-id-meta":"","stick-header-meta":"","header-above-stick-meta":"","header-main-stick-meta":"","header-below-stick-meta":"","astra-migrate-meta-layouts":"set","ast-page-background-enabled":"default","ast-page-background-meta":{"desktop":{"background-color":"","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""},"tablet":{"background-color":"","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""},"mobile":{"background-color":"","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""}},"ast-content-background-meta":{"desktop":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""},"tablet":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""},"mobile":{"background-color":"var(--ast-global-color-5)","background-image":"","background-repeat":"repeat","background-position":"center center","background-size":"auto","background-attachment":"scroll","background-type":"","background-media":"","overlay-type":"","overlay-color":"","overlay-opacity":"","overlay-gradient":""}},"footnotes":""},"categories":[72],"tags":[],"class_list":["post-8938","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-education-fr"],"aioseo_notices":[],"_links":{"self":[{"href":"https:\/\/loeysdietzcanada.org\/fr\/wp-json\/wp\/v2\/posts\/8938","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/loeysdietzcanada.org\/fr\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/loeysdietzcanada.org\/fr\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/loeysdietzcanada.org\/fr\/wp-json\/wp\/v2\/users\/4"}],"replies":[{"embeddable":true,"href":"https:\/\/loeysdietzcanada.org\/fr\/wp-json\/wp\/v2\/comments?post=8938"}],"version-history":[{"count":4,"href":"https:\/\/loeysdietzcanada.org\/fr\/wp-json\/wp\/v2\/posts\/8938\/revisions"}],"predecessor-version":[{"id":8942,"href":"https:\/\/loeysdietzcanada.org\/fr\/wp-json\/wp\/v2\/posts\/8938\/revisions\/8942"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/loeysdietzcanada.org\/fr\/wp-json\/wp\/v2\/media\/8924"}],"wp:attachment":[{"href":"https:\/\/loeysdietzcanada.org\/fr\/wp-json\/wp\/v2\/media?parent=8938"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/loeysdietzcanada.org\/fr\/wp-json\/wp\/v2\/categories?post=8938"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/loeysdietzcanada.org\/fr\/wp-json\/wp\/v2\/tags?post=8938"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}