{"id":1763,"date":"2022-07-18T16:51:53","date_gmt":"2022-07-18T20:51:53","guid":{"rendered":"https:\/\/loeysdietzcanada.org\/?page_id=1763"},"modified":"2025-01-20T11:48:58","modified_gmt":"2025-01-20T16:48:58","slug":"traitement","status":"publish","type":"page","link":"https:\/\/loeysdietzcanada.org\/fr\/syndrome-de-loeys-dietz\/traitement\/","title":{"rendered":"Traitement"},"content":{"rendered":"\t\t<div data-elementor-type=\"wp-page\" data-elementor-id=\"1763\" class=\"elementor elementor-1763 elementor-693\" data-elementor-post-type=\"page\">\n\t\t\t\t\t\t<section data-particle_enable=\"false\" data-particle-mobile-disabled=\"false\" class=\"elementor-section elementor-top-section elementor-element elementor-element-1e861717 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"1e861717\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-4dadb7f5\" data-id=\"4dadb7f5\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-100bc0e8 elementor-widget elementor-widget-heading\" data-id=\"100bc0e8\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h1 class=\"elementor-heading-title elementor-size-default\">Traitement<\/h1>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section data-particle_enable=\"false\" data-particle-mobile-disabled=\"false\" class=\"elementor-section elementor-top-section elementor-element elementor-element-2f236ef elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"2f236ef\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-0883c57\" data-id=\"0883c57\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-447b734 elementor-widget elementor-widget-heading\" data-id=\"447b734\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Philosophies de traitement pour le syndrome de Loeys-Dietz<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section data-particle_enable=\"false\" data-particle-mobile-disabled=\"false\" class=\"elementor-section elementor-top-section elementor-element elementor-element-4b72940 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"4b72940\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t\t<div class=\"elementor-background-overlay\"><\/div>\n\t\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-3cd6626\" data-id=\"3cd6626\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-341f357 elementor-view-default elementor-widget elementor-widget-icon\" data-id=\"341f357\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"icon.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-icon-wrapper\">\n\t\t\t<div class=\"elementor-icon\">\n\t\t\t<i aria-hidden=\"true\" class=\"fas fa-child\"><\/i>\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-c63d179 elementor-widget elementor-widget-heading\" data-id=\"c63d179\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Une approche individualis\u00e9e<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-9889b00 elementor-widget elementor-widget-text-editor\" data-id=\"9889b00\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Le traitement et la prise en charge diff\u00e8rent d\u2019une personne \u00e0 l\u2019autre car le SLD peut affecter les individus de mani\u00e8res vari\u00e9es.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-c0b3178\" data-id=\"c0b3178\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-8cea194 elementor-view-default elementor-widget elementor-widget-icon\" data-id=\"8cea194\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"icon.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-icon-wrapper\">\n\t\t\t<div class=\"elementor-icon\">\n\t\t\t<i aria-hidden=\"true\" class=\"fas fa-clinic-medical\"><\/i>\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-0c848ff elementor-widget elementor-widget-heading\" data-id=\"0c848ff\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">Soins multidisciplinaires<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-dfc3b8d elementor-widget elementor-widget-text-editor\" data-id=\"dfc3b8d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p><span style=\"font-weight: 400;\">Le syndrome de Loeys-Dietz touche plusieurs syst\u00e8mes corporels et est donc mieux pris en charge par une \u00e9quipe <\/span><b>multidisciplinaire<\/b><span style=\"font-weight: 400;\"> de professionnels de la sant\u00e9.<\/span><\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-2baa5ff elementor-widget elementor-widget-eael-adv-accordion\" data-id=\"2baa5ff\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"eael-adv-accordion.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t            <div class=\"eael-adv-accordion\" id=\"eael-adv-accordion-2baa5ff\" data-scroll-on-click=\"no\" data-scroll-speed=\"300\" data-accordion-id=\"2baa5ff\" data-accordion-type=\"accordion\" data-toogle-speed=\"300\">\n            <div class=\"eael-accordion-list\">\n\t\t\t\t\t<div id=\"membres-de-lquipe\" class=\"elementor-tab-title eael-accordion-header\" tabindex=\"0\" data-tab=\"1\" aria-controls=\"elementor-tab-content-4571\"><span class=\"eael-advanced-accordion-icon-closed\"><i aria-hidden=\"true\" class=\"fa-accordion-icon fas fa-plus\"><\/i><\/span><span class=\"eael-advanced-accordion-icon-opened\"><i aria-hidden=\"true\" class=\"fa-accordion-icon fas fa-minus\"><\/i><\/span><span class=\"eael-accordion-tab-title\">Membres de l'\u00e9quipe<\/span><\/div><div id=\"elementor-tab-content-4571\" class=\"eael-accordion-content clearfix\" data-tab=\"1\" aria-labelledby=\"membres-de-lquipe\"><p><span style=\"font-weight: 400\">Cette <strong>\u00e9quipe<\/strong> peut inclure un prestataire de soins primaires, un cardiologue, un orthop\u00e9diste, un g\u00e9n\u00e9ticien clinique, un ophtalmologue, un chirurgien cardiothoracique, un professionnel de la sant\u00e9 mentale et tout autre sp\u00e9cialiste n\u00e9cessaire au traitement des sympt\u00f4mes du patient.<\/span><\/p><\/div>\n\t\t\t\t\t<\/div><div class=\"eael-accordion-list\">\n\t\t\t\t\t<div id=\"coordonnateur-de-soins\" class=\"elementor-tab-title eael-accordion-header\" tabindex=\"0\" data-tab=\"2\" aria-controls=\"elementor-tab-content-4572\"><span class=\"eael-advanced-accordion-icon-closed\"><i aria-hidden=\"true\" class=\"fa-accordion-icon fas fa-plus\"><\/i><\/span><span class=\"eael-advanced-accordion-icon-opened\"><i aria-hidden=\"true\" class=\"fa-accordion-icon fas fa-minus\"><\/i><\/span><span class=\"eael-accordion-tab-title\">Coordonnateur de soins<\/span><\/div><div id=\"elementor-tab-content-4572\" class=\"eael-accordion-content clearfix\" data-tab=\"2\" aria-labelledby=\"coordonnateur-de-soins\"><p><span style=\"font-weight: 400\">En plus d&#8217;une \u00e9quipe de sp\u00e9cialistes travaillant en collaboration, les patients b\u00e9n\u00e9ficient d&#8217;un <\/span><b>coordonnateur de soins<\/b><span style=\"font-weight: 400\"> qui peut d\u00e9fendre les int\u00e9r\u00eats du patient ainsi qu\u2019organiser et suivre les soins sp\u00e9cialis\u00e9s. En fonction du niveau de soins requis et des services de soins de sant\u00e9 disponibles, le coordonnateur de soins peut \u00eatre un prestataire de soins primaires, un professionnel de la g\u00e9n\u00e9tique, le patient, un parent ou un soignant du patient.<\/span><\/p><\/div>\n\t\t\t\t\t<\/div><\/div>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t<div class=\"elementor-column elementor-col-33 elementor-top-column elementor-element elementor-element-7669197\" data-id=\"7669197\" data-element_type=\"column\" data-e-type=\"column\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-3d381a9 elementor-view-default elementor-widget elementor-widget-icon\" data-id=\"3d381a9\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"icon.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-icon-wrapper\">\n\t\t\t<div class=\"elementor-icon\">\n\t\t\t<i aria-hidden=\"true\" class=\"fas fa-hands-helping\"><\/i>\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-8aaaf9f elementor-widget elementor-widget-heading\" data-id=\"8aaaf9f\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h3 class=\"elementor-heading-title elementor-size-default\">La prise de d\u00e9cision partag\u00e9e<\/h3>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-e750e16 elementor-widget elementor-widget-text-editor\" data-id=\"e750e16\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>La prise de d\u00e9cision partag\u00e9e\u00a0entre les professionnels de la sant\u00e9, les patients et les familles tient compte des besoins et des souhaits du patient, aide le patient et sa famille \u00e0 comprendre la maladie et les options de traitement, et est particuli\u00e8rement importante pour des \u00e9v\u00e9nements tels que la chirurgie ou la grossesse.<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section data-particle_enable=\"false\" data-particle-mobile-disabled=\"false\" class=\"elementor-section elementor-top-section elementor-element elementor-element-00aa372 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"00aa372\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-b0f9be1\" data-id=\"b0f9be1\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-9e8d120 elementor-widget elementor-widget-text-editor\" data-id=\"9e8d120\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"text-editor.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<p>Il est recommand\u00e9 de consulter avec un professionnel de la sant\u00e9 de vos probl\u00e8mes de sant\u00e9, ainsi que des options de traitement et de gestion.\u00a0<\/p>\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-1e53e28 elementor-align-center elementor-widget elementor-widget-button\" data-id=\"1e53e28\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"button.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t\t\t<div class=\"elementor-button-wrapper\">\n\t\t\t\t\t<a class=\"elementor-button elementor-button-link elementor-size-sm\" href=\"https:\/\/loeysdietzcanada.org\/fr\/soutien-aux-patients\/ou-trouver-une-clinique\/\" target=\"_blank\">\n\t\t\t\t\t\t<span class=\"elementor-button-content-wrapper\">\n\t\t\t\t\t\t<span class=\"elementor-button-icon\">\n\t\t\t\t<i aria-hidden=\"true\" class=\"fas fa-long-arrow-alt-right\"><\/i>\t\t\t<\/span>\n\t\t\t\t\t\t\t\t\t<span class=\"elementor-button-text\">Trouvez une clinique<\/span>\n\t\t\t\t\t<\/span>\n\t\t\t\t\t<\/a>\n\t\t\t\t<\/div>\n\t\t\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<section data-particle_enable=\"false\" data-particle-mobile-disabled=\"false\" class=\"elementor-section elementor-top-section elementor-element elementor-element-226065d5 elementor-section-boxed elementor-section-height-default elementor-section-height-default\" data-id=\"226065d5\" data-element_type=\"section\" data-e-type=\"section\" data-settings=\"{&quot;background_background&quot;:&quot;classic&quot;}\">\n\t\t\t\t\t\t<div class=\"elementor-container elementor-column-gap-default\">\n\t\t\t\t\t<div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-1370c628\" data-id=\"1370c628\" data-element_type=\"column\" data-e-type=\"column\">\n\t\t\t<div class=\"elementor-widget-wrap elementor-element-populated\">\n\t\t\t\t\t\t<div class=\"elementor-element elementor-element-2f9b1e6 elementor-widget elementor-widget-heading\" data-id=\"2f9b1e6\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"heading.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t<h2 class=\"elementor-heading-title elementor-size-default\">Types de traitement et de soins pour le syndrome de Loeys-Dietz<\/h2>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-4de271b elementor-widget elementor-widget-spacer\" data-id=\"4de271b\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-17c677d elementor-widget elementor-widget-eael-adv-accordion\" data-id=\"17c677d\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"eael-adv-accordion.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t            <div class=\"eael-adv-accordion\" id=\"eael-adv-accordion-17c677d\" data-scroll-on-click=\"no\" data-scroll-speed=\"300\" data-accordion-id=\"17c677d\" data-accordion-type=\"accordion\" data-toogle-speed=\"300\">\n            <div class=\"eael-accordion-list\">\n\t\t\t\t\t<div id=\"mdicaments\" class=\"elementor-tab-title eael-accordion-header\" tabindex=\"0\" data-tab=\"1\" aria-controls=\"elementor-tab-content-2491\"><span class=\"eael-advanced-accordion-icon-closed\"><\/span><span class=\"eael-advanced-accordion-icon-opened\"><\/span><span class=\"eael-accordion-tab-title\">M\u00e9dicaments<\/span><i aria-hidden=\"true\" class=\"fa-toggle fas fa-plus\"><\/i><\/div><div id=\"elementor-tab-content-2491\" class=\"eael-accordion-content clearfix\" data-tab=\"1\" aria-labelledby=\"mdicaments\"><p><span style=\"font-weight: 400\">Des m\u00e9dicaments peuvent \u00eatre prescrits pour diminuer la pression art\u00e9rielle et la fr\u00e9quence cardiaque afin de r\u00e9duire le stress sur les art\u00e8res (vaisseaux sanguins transportant le sang du c\u0153ur vers le corps) et l&#8217;aorte (art\u00e8re reli\u00e9e au c\u0153ur). <\/span><\/p><p><span style=\"font-weight: 400\">De nombreuses personnes atteintes de SLD prennent des m\u00e9dicaments appel\u00e9s <\/span><b>antagonistes des r\u00e9cepteurs de l&#8217;angiotensine<\/b><span style=\"font-weight: 400\"> (ARA) (Losartan, Candesartan, Irbesartan, etc.) et des <\/span><b>b\u00eata-bloquants<\/b><span style=\"font-weight: 400\"> (Atenolol, Propanolol, Metoprolol, etc.). Dans des \u00e9tudes de recherche, il a \u00e9t\u00e9 d\u00e9montr\u00e9 que les ARA diminuent la croissance des an\u00e9vrismes chez les souris atteintes de SLD. <\/span><\/p><p><span style=\"font-weight: 400\">Les m\u00e9dicaments doivent g\u00e9n\u00e9ralement \u00eatre pris selon une titration optimale (une dose personnalis\u00e9e qui vise \u00e0 maximiser les effets b\u00e9n\u00e9fiques du m\u00e9dicament et \u00e0 minimiser ses effets secondaires) et poursuivis apr\u00e8s une chirurgie vasculaire.<\/span><\/p><p>En savoir plus ici : <a href=\"https:\/\/loeysdietzcanada.org\/fr\/syndrome-de-loeys-dietz\/medicaments\/\" target=\"_blank\" rel=\"noopener\">Le syndrome de Loeys-Dietz et les m\u00e9dicaments<\/a>\u00a0<\/p><\/div>\n\t\t\t\t\t<\/div><div class=\"eael-accordion-list\">\n\t\t\t\t\t<div id=\"imagerie-vasculaire\" class=\"elementor-tab-title eael-accordion-header\" tabindex=\"0\" data-tab=\"2\" aria-controls=\"elementor-tab-content-2492\"><span class=\"eael-advanced-accordion-icon-closed\"><\/span><span class=\"eael-advanced-accordion-icon-opened\"><\/span><span class=\"eael-accordion-tab-title\">Imagerie vasculaire<\/span><i aria-hidden=\"true\" class=\"fa-toggle fas fa-plus\"><\/i><\/div><div id=\"elementor-tab-content-2492\" class=\"eael-accordion-content clearfix\" data-tab=\"2\" aria-labelledby=\"imagerie-vasculaire\"><p><span style=\"font-weight: 400\">L&#8217;objectif de l&#8217;imagerie vasculaire est de rep\u00e9rer et de surveiller les an\u00e9vrismes et les dissections (ruptures d&#8217;art\u00e8res). <\/span><\/p><p><span style=\"font-weight: 400\">Il est recommand\u00e9 d&#8217;effectuer chaque ann\u00e9e une \u00e9chocardiographie de l&#8217;aorte et, apr\u00e8s le diagnostic, une imagerie de la t\u00eate au pelvis (t\u00eate, cou, poitrine, pelvis et abdomen) par une <\/span><b>angiographie par TDM <\/b>(<span style=\"font-weight: 400\">Tomodensitom\u00e9trie)<\/span> <span style=\"font-weight: 400\">\u00a0ou <\/span><b>ARM<\/b><span style=\"font-weight: 400\"> (angiographie par r\u00e9sonance magn\u00e9tique). Les personnes atteintes de SLD doivent ensuite subir une imagerie de la t\u00eate au pelvis au moins une fois tous les deux ans. \u00c9tant donn\u00e9 que certaines petites art\u00e8res de la t\u00eate et du cou peuvent \u00eatre difficiles \u00e0 surveiller par ARM, les personnes qui re\u00e7oivent des images par ARM devraient \u00e9galement recevoir r\u00e9guli\u00e8rement des images par tomodensitom\u00e9trie apr\u00e8s quelques ARM. <\/span><\/p><p><span style=\"font-weight: 400\">Les personnes devraient rencontrer un cardiologue qui peut \u00e9valuer le taux de croissance et la taille des an\u00e9vrismes et recommander une fr\u00e9quence d&#8217;imagerie personnalis\u00e9e.<\/span><\/p><\/div>\n\t\t\t\t\t<\/div><div class=\"eael-accordion-list\">\n\t\t\t\t\t<div id=\"imagerie-de-la-colonne-cervicale\" class=\"elementor-tab-title eael-accordion-header\" tabindex=\"0\" data-tab=\"3\" aria-controls=\"elementor-tab-content-2493\"><span class=\"eael-advanced-accordion-icon-closed\"><\/span><span class=\"eael-advanced-accordion-icon-opened\"><\/span><span class=\"eael-accordion-tab-title\">Imagerie de la colonne cervicale<\/span><i aria-hidden=\"true\" class=\"fa-toggle fas fa-plus\"><\/i><\/div><div id=\"elementor-tab-content-2493\" class=\"eael-accordion-content clearfix\" data-tab=\"3\" aria-labelledby=\"imagerie-de-la-colonne-cervicale\"><p><span style=\"font-weight: 400\">Une radiographie de la colonne cervicale en position d&#8217;extension et de flexion est recommand\u00e9e avant toute intervention chirurgicale, intubation ou manipulation du cou. <\/span><\/p><p><span style=\"font-weight: 400\">Si la radiographie d\u00e9tecte une instabilit\u00e9 ou des anomalies de la colonne cervicale, il faut consulter un orthop\u00e9diste et, dans de cas rares, une chirurgie de fusion de la colonne cervicale peut \u00eatre n\u00e9cessaire pour joindre les vert\u00e8bres.<\/span><\/p><\/div>\n\t\t\t\t\t<\/div><div class=\"eael-accordion-list\">\n\t\t\t\t\t<div id=\"chirurgie-vasculaire\" class=\"elementor-tab-title eael-accordion-header\" tabindex=\"0\" data-tab=\"4\" aria-controls=\"elementor-tab-content-2494\"><span class=\"eael-advanced-accordion-icon-closed\"><\/span><span class=\"eael-advanced-accordion-icon-opened\"><\/span><span class=\"eael-accordion-tab-title\">Chirurgie vasculaire<\/span><i aria-hidden=\"true\" class=\"fa-toggle fas fa-plus\"><\/i><\/div><div id=\"elementor-tab-content-2494\" class=\"eael-accordion-content clearfix\" data-tab=\"4\" aria-labelledby=\"chirurgie-vasculaire\"><p><span style=\"font-weight: 400\">La chirurgie vasculaire est pratiqu\u00e9e chez les personnes atteintes du SLD pour r\u00e9parer les manifestations du syst\u00e8me circulatoire. <\/span><\/p><p><span style=\"font-weight: 400\">Elle est <\/span><b>largement recommand\u00e9e<\/b><span style=\"font-weight: 400\"> en tant que chirurgie pr\u00e9ventive pour les patients atteints du SLD pr\u00e9sentant une dilatation rapide des art\u00e8res (vaisseaux sanguins qui transportent le sang du c\u0153ur vers le reste du corps), une dilatation rapide de l&#8217;aorte (art\u00e8re en forme de canne \u00e0 sucre qui commence au sommet du c\u0153ur et se termine dans l&#8217;abdomen), ou des ant\u00e9c\u00e9dents familiaux prononc\u00e9s de dissection art\u00e9rielle. <\/span><\/p><p><span style=\"font-weight: 400\">La chirurgie vasculaire <\/span><b>pr\u00e9ventive<\/b><span style=\"font-weight: 400\"> ou prophylactique vise \u00e0 emp\u00eacher les dilatations art\u00e9rielles et les an\u00e9vrismes (renflements anormaux des art\u00e8res) de grossir et de se diss\u00e9quer (grossir suffisamment pour d\u00e9chirer l&#8217;art\u00e8re). <\/span><\/p><p><span style=\"font-weight: 400\">La chirurgie vasculaire est \u00e9galement pratiqu\u00e9e dans des situations <\/span><b>d&#8217;urgence<\/b><span style=\"font-weight: 400\">, comme dans le cas de dissections art\u00e9rielles. <\/span><\/p><p><span style=\"font-weight: 400\">En savoir plus sur <a href=\"https:\/\/loeysdietzcanada.org\/fr\/soutien-aux-patients\/preparation-intervention-chirurgicale\/\" target=\"_blank\" rel=\"noopener\">les types de chirurgie vasculaire et les conseils aux patients et aux parents.<\/a><\/span><\/p><\/div>\n\t\t\t\t\t<\/div><div class=\"eael-accordion-list\">\n\t\t\t\t\t<div id=\"restrictions-dexercice\" class=\"elementor-tab-title eael-accordion-header\" tabindex=\"0\" data-tab=\"5\" aria-controls=\"elementor-tab-content-2495\"><span class=\"eael-advanced-accordion-icon-closed\"><\/span><span class=\"eael-advanced-accordion-icon-opened\"><\/span><span class=\"eael-accordion-tab-title\">Restrictions d'exercice<\/span><i aria-hidden=\"true\" class=\"fa-toggle fas fa-plus\"><\/i><\/div><div id=\"elementor-tab-content-2495\" class=\"eael-accordion-content clearfix\" data-tab=\"5\" aria-labelledby=\"restrictions-dexercice\"><p><span style=\"font-weight: 400\">Les restrictions d&#8217;exercice visent \u00e0 r\u00e9duire la pression exerc\u00e9e sur le syst\u00e8me cardiovasculaire, \u00e0 minimiser la croissance des an\u00e9vrismes et \u00e0 \u00e9viter les dissections. <\/span><\/p><p><span style=\"font-weight: 400\">Les personnes atteintes du SLD sont encourag\u00e9es \u00e0 pratiquer des exercices d&#8217;a\u00e9robie (comme la natation, le jogging, la randonn\u00e9e et le v\u00e9lo) avec mod\u00e9ration. Un niveau d&#8217;activit\u00e9 mod\u00e9r\u00e9 signifie que vous pouvez avoir une conversation tout en faisant de l&#8217;exercice, peut contribuer \u00e0 r\u00e9duire la pression art\u00e9rielle et la fr\u00e9quence cardiaque, et ainsi \u00e0 am\u00e9liorer la sant\u00e9 mentale et l&#8217;humeur. <\/span><\/p><p><span style=\"font-weight: 400\">Il est recommand\u00e9 aux personnes atteintes du SLD <\/span><span style=\"font-weight: 400\"><strong>d&#8217;\u00e9viter<\/strong> de :<\/span><\/p><ul><li><span style=\"font-weight: 400\">faire de l&#8217;exercice jusqu&#8217;\u00e0 l&#8217;\u00e9puisement<\/span><\/li><li><span style=\"font-weight: 400\">de solliciter les muscles par des exercices de poids corporel (pompes, redressements assis et tractions) et de soulever des poids, <\/span><\/li><li><span style=\"font-weight: 400\">de pratiquer des sports de comp\u00e9tition et de contact<\/span><\/li><li><span style=\"font-weight: 400\">d&#8217;effectuer des mouvements d&#8217;hyperextension des articulations ou de provoquer des l\u00e9sions ou des douleurs articulaires. <\/span><\/li><\/ul><p><span style=\"font-weight: 400\">Un cardiologue peut utiliser ces directives pour expliquer plus en d\u00e9tail le type et l&#8217;intensit\u00e9 d&#8217;exercice qui conviennent \u00e0 chaque individu.<\/span><\/p><p>En savoir plus sur <a href=\"https:\/\/loeysdietzcanada.org\/fr\/soutien-aux-patients\/bien-vivre-avec-le-sld\/\" target=\"_blank\" rel=\"noopener\">l&#8217;exercise et le syndrome de Loeys-Dietz.\u00a0<\/a><\/p><\/div>\n\t\t\t\t\t<\/div><div class=\"eael-accordion-list\">\n\t\t\t\t\t<div id=\"orthopdie\" class=\"elementor-tab-title eael-accordion-header\" tabindex=\"0\" data-tab=\"6\" aria-controls=\"elementor-tab-content-2496\"><span class=\"eael-advanced-accordion-icon-closed\"><\/span><span class=\"eael-advanced-accordion-icon-opened\"><\/span><span class=\"eael-accordion-tab-title\">Orthop\u00e9die<\/span><i aria-hidden=\"true\" class=\"fa-toggle fas fa-plus\"><\/i><\/div><div id=\"elementor-tab-content-2496\" class=\"eael-accordion-content clearfix\" data-tab=\"6\" aria-labelledby=\"orthopdie\"><p><span style=\"font-weight: 400\">Le traitement orthop\u00e9dique du SLD comprend l&#8217;attelle, le pl\u00e2tre, les \u00e9tirements, les orth\u00e8ses et la chirurgie orthop\u00e9dique. <\/span><\/p><p><span style=\"font-weight: 400\">En savoir plus sur la <a href=\"https:\/\/loeysdietzcanada.org\/fr\/soutien-aux-patients\/preparation-intervention-chirurgicale\/\" target=\"_blank\" rel=\"noopener\">chirurgie du pied bot, du pectus carinatum et du pectus excavatum<\/a>.<\/span><\/p><\/div>\n\t\t\t\t\t<\/div><div class=\"eael-accordion-list\">\n\t\t\t\t\t<div id=\"allergies\" class=\"elementor-tab-title eael-accordion-header\" tabindex=\"0\" data-tab=\"7\" aria-controls=\"elementor-tab-content-2497\"><span class=\"eael-advanced-accordion-icon-closed\"><\/span><span class=\"eael-advanced-accordion-icon-opened\"><\/span><span class=\"eael-accordion-tab-title\">Allergies<\/span><i aria-hidden=\"true\" class=\"fa-toggle fas fa-plus\"><\/i><\/div><div id=\"elementor-tab-content-2497\" class=\"eael-accordion-content clearfix\" data-tab=\"7\" aria-labelledby=\"allergies\"><p><span style=\"font-weight: 400\">Les personnes atteintes du syndrome de Loeys-Dietz sont plus susceptibles que la population g\u00e9n\u00e9rale de souffrir d&#8217;une maladie allergique telle qu&#8217;une allergie alimentaire, une allergie environnementale, de l&#8217;ecz\u00e9ma, de l&#8217;asthme, une \u0153sophagite \u00e0 \u00e9osinophiles, et une gastrite \u00e0 \u00e9osinophiles. <\/span><\/p><p><span style=\"font-weight: 400\">Le traitement varie en fonction de la personne et de son \u00e9tat, mais il peut consister \u00e0 limiter l&#8217;exposition aux facteurs d\u00e9clenchants des allergies alimentaires et environnementales ainsi que l&#8217;asthme. <\/span><\/p><p><span style=\"font-weight: 400\"><strong>L&#8217;ecz\u00e9ma<\/strong> peut \u00eatre trait\u00e9 avec des cr\u00e8mes hydratantes, des m\u00e9dicaments et des changements dans l&#8217;alimentation et du mode de vie. <\/span><\/p><p><span style=\"font-weight: 400\">Les <strong>r\u00e9actions anaphylactiques<\/strong> (graves) doivent \u00eatre trait\u00e9es imm\u00e9diatement \u00e0 l&#8217;aide d&#8217;un injecteur d&#8217;\u00e9pin\u00e9phrine et d&#8217;un appel aux services m\u00e9dicaux d&#8217;urgence comme le 911. En raison de son effet sur le syst\u00e8me circulatoire, un injecteur d&#8217;\u00e9pin\u00e9phrine ne doit \u00eatre utilis\u00e9 que pour traiter les r\u00e9actions anaphylactiques ou les sympt\u00f4mes mettant la vie en danger (et non les sympt\u00f4mes l\u00e9gers) chez les personnes atteintes du SLD. Demandez \u00e0 votre cardiologue et\/ou \u00e0 votre allergologue de vous dire exactement quand utiliser un injecteur d&#8217;\u00e9pin\u00e9phrine. <\/span><\/p><p><span style=\"font-weight: 400\">Les <strong>sympt\u00f4mes gastro-intestinaux li\u00e9s aux allergies<\/strong> comprennent les douleurs abdominales, la diarrh\u00e9e, la sensation de nourriture coinc\u00e9e dans la gorge et la difficult\u00e9 \u00e0 prendre et \u00e0 maintenir du poids. Les personnes concern\u00e9es peuvent avoir besoin d&#8217;un traitement m\u00e9dicamenteux et\/ou d&#8217;une sonde d&#8217;alimentation.<\/span><\/p><\/div>\n\t\t\t\t\t<\/div><div class=\"eael-accordion-list\">\n\t\t\t\t\t<div id=\"-la-planification-familiale\" class=\"elementor-tab-title eael-accordion-header\" tabindex=\"0\" data-tab=\"8\" aria-controls=\"elementor-tab-content-2498\"><span class=\"eael-accordion-tab-title\"> La planification familiale<\/span><i aria-hidden=\"true\" class=\"fa-toggle fas fa-plus\"><\/i><\/div><div id=\"elementor-tab-content-2498\" class=\"eael-accordion-content clearfix\" data-tab=\"8\" aria-labelledby=\"-la-planification-familiale\"><div class=\"page\"><div class=\"section\"><div class=\"layoutArea\"><div class=\"column\"><p>La planification familiale permet aux personnes de de\u0301terminer le nombre d&#8217;enfants qu&#8217;elles souhaitent avoir. Il est essentiel que vous communiquiez avec un professionnel des soins de sante\u0301 au stade de la pre\u0301conception afin d&#8217;e\u0301valuer votre e\u0301tat de sante\u0301 et de discuter des options qui s&#8217;offrent a\u0300 vous.<\/p><section class=\"elementor-section elementor-top-section elementor-element elementor-element-8fa07bb elementor-section-boxed elementor-section-height-default elementor-section-height-default\"><div class=\"elementor-container elementor-column-gap-default\"><div class=\"elementor-column elementor-col-100 elementor-top-column elementor-element elementor-element-14e1050\"><div class=\"elementor-widget-wrap elementor-element-populated\"><div class=\"elementor-element elementor-element-26ad597 elementor-widget elementor-widget-text-editor\"><div class=\"elementor-widget-container\"><p>Le livret sur la planification familiale avec le SLD est une ressource compl\u00e8te con\u00e7ue pour donner aux individus et aux familles les connaissances n\u00e9cessaires pour prendre des d\u00e9cisions \u00e9clair\u00e9es. Ce guide va au-del\u00e0 des informations fondamentales, abordant des aspects sp\u00e9cifiques li\u00e9s au syndrome de Loeys-Dietz et \u00e0 la planification familiale, \u00e0 la grossesse, \u00e0 l\u2019accouchement et aux soins post-partum.<\/p><div>\u00a0<\/div><div><div><strong>Ce qui est inclus ?<\/strong><\/div><div>\u00a0<\/div><ul><li><strong>Qu\u2019est-ce que la planification familiale ?<\/strong><\/li><li>Une introduction au concept et \u00e0 l\u2019importance de la planification familiale.<\/li><li><strong>Le SLD et la grossesse<\/strong><ul><li>Une plong\u00e9e approfondie dans l\u2019intersection du SLD et la grossesse.<\/li><\/ul><\/li><li><strong>Liste de contr\u00f4le avant la conception<\/strong><ul><li>\u00c9tapes pratiques \u00e0 consid\u00e9rer avant la conception, assurant un parcours bien pr\u00e9par\u00e9.<\/li><\/ul><\/li><li><strong>\u00c9valuation m\u00e9dicale de la m\u00e8re<\/strong><ul><li>Compr\u00e9hension des \u00e9valuations m\u00e9dicales cruciales pour la sant\u00e9 maternelle pendant la grossesse.<\/li><\/ul><\/li><li><strong>M\u00e9dicaments courants pour le SLD pendant la grossesse<\/strong><ul><li>Aper\u00e7u des m\u00e9dicaments couramment utilis\u00e9s pour traiter les manifestations du SLD et leur gestion pendant la grossesse.<\/li><\/ul><\/li><li><strong>Risques maternels et consid\u00e9rations relatives \u00e0 la progeniture<\/strong><ul><li>Une exploration r\u00e9fl\u00e9chie des risques et des consid\u00e9rations pendant la grossesse.<\/li><\/ul><\/li><li><strong>Grossesse<\/strong><ul><li>\u00c9tapes pratiques \u00e0 consid\u00e9rer \u00e0 chaque trimestre.<\/li><\/ul><\/li><li><strong>Logistique de l\u2019accouchement\u00a0<\/strong><ul><li>Orientation sur la navigation des aspects logistiques de l\u2019accouchement\u00a0<\/li><\/ul><\/li><li><strong>Post-partum<\/strong><ul><li>Orientation pour naviguer la p\u00e9riode du post-partum.<\/li><\/ul><\/li><li><strong>La maternit\u00e9 de substitution<\/strong><ul><li>Exploration de l\u2019option de la maternit\u00e9 de substitution et ses consid\u00e9rations.<\/li><\/ul><\/li><li><strong>Pr\u00e9servation de la fertilit\u00e9<\/strong><ul><li>Aper\u00e7u de la pr\u00e9servation de la fertilit\u00e9 pour les personnes atteintes du SLD.<\/li><\/ul><\/li><li><strong>FIV, MIV et IIU<\/strong><ul><li>Aper\u00e7u des technologies de procr\u00e9ation assist\u00e9e et de leur pertinence.<\/li><\/ul><\/li><li><strong>Adoption<\/strong><ul><li>Consid\u00e9rations et id\u00e9es pour ceux qui explorent la voie de l\u2019adoption.<\/li><\/ul><\/li><\/ul><\/div><\/div><\/div><\/div><\/div><\/div><\/section><section class=\"elementor-section elementor-top-section elementor-element elementor-element-266dc02 elementor-section-boxed elementor-section-height-default elementor-section-height-default\"><div class=\"elementor-container elementor-column-gap-default\"><div class=\"elementor-column elementor-col-50 elementor-top-column elementor-element elementor-element-8658fd3\"><div class=\"elementor-widget-wrap elementor-element-populated\"><div class=\"elementor-element elementor-element-5d9ad97 elementor-widget__width-initial elementor-widget elementor-widget-text-editor\"><div class=\"elementor-widget-container\"><p><strong>Comment obtenir votre exemplaire<\/strong><\/p><p><a href=\"https:\/\/loeysdietzcanada.org\/wp-content\/uploads\/2023\/12\/FINAL-FR-COPY-LDS-Family-Planning.pdf\" target=\"_blank\" rel=\"noopener\">T\u00e9l\u00e9chargez cette ressource inestimable gratuitement ici.<\/a><\/p><\/div><\/div><\/div><\/div><\/div><\/section><\/div><\/div><\/div><\/div><\/div>\n\t\t\t\t\t<\/div><div class=\"eael-accordion-list\">\n\t\t\t\t\t<div id=\"prparation-aux-cas-durgence\" class=\"elementor-tab-title eael-accordion-header\" tabindex=\"0\" data-tab=\"9\" aria-controls=\"elementor-tab-content-2499\"><span class=\"eael-accordion-tab-title\">Pr\u00e9paration aux cas d'urgence<\/span><i aria-hidden=\"true\" class=\"fa-toggle fas fa-plus\"><\/i><\/div><div id=\"elementor-tab-content-2499\" class=\"eael-accordion-content clearfix\" data-tab=\"9\" aria-labelledby=\"prparation-aux-cas-durgence\"><p style=\"font-weight: 400\">Lorsque vous vivez avec un membre de votre famille atteint du syndrome de Loeys-Dietz ou que vous \u00eates atteint du syndrome de Loeys-Dietz, une situation d&#8217;urgence peut survenir \u00e0 tout moment. Le livret sur la pr\u00e9paration aux situations d&#8217;urgence li\u00e9es au syndrome de Loeys-Dietz vise \u00e0 fournir aux individus et aux familles les outils n\u00e9cessaires pour se pr\u00e9parer \u00e0 une \u00e9ventuelle situation d&#8217;urgence.<\/p><p style=\"font-weight: 400\"><strong>De quoi discutons-nous dans ce livret?<\/strong><\/p><ul><li>Signes et sympt\u00f4mes d&#8217;urgence<\/li><li>Autres situations d&#8217;urgence<\/li><li>Informations vitales pour les m\u00e9decins<\/li><li>Pr\u00e9paration aux situations d&#8217;urgence<\/li><li>Pr\u00e9paration aux situations d&#8217;urgence ax\u00e9e sur la famille<\/li><li>Dispositifs d&#8217;alerte m\u00e9dicale portables<\/li><li>Directives avanc\u00e9es<\/li><li>Sensibilisation<\/li><li>Suggestions d&#8217;experts<\/li><\/ul><p style=\"font-weight: 400\"><strong>Comment obtenir votre exemplaire :<\/strong><\/p><p><a href=\"https:\/\/loeysdietzcanada.org\/wp-content\/uploads\/2025\/01\/LDS-EMERGENCY-PREPAREDNESS_FR.pdf\" target=\"_blank\" rel=\"noopener\"><span style=\"font-weight: 400\">T\u00e9l\u00e9chargez cette ressource inestimable gratuitement ici.<\/span><\/a><\/p><\/div>\n\t\t\t\t\t<\/div><\/div>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-1aeae09 elementor-widget elementor-widget-spacer\" data-id=\"1aeae09\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-fcfaf9a elementor-widget elementor-widget-spacer\" data-id=\"fcfaf9a\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"spacer.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t\t\t<div class=\"elementor-spacer\">\n\t\t\t<div class=\"elementor-spacer-inner\"><\/div>\n\t\t<\/div>\n\t\t\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t<div class=\"elementor-element elementor-element-c110539 elementor-widget elementor-widget-eael-adv-accordion\" data-id=\"c110539\" data-element_type=\"widget\" data-e-type=\"widget\" data-widget_type=\"eael-adv-accordion.default\">\n\t\t\t\t<div class=\"elementor-widget-container\">\n\t\t\t\t\t            <div class=\"eael-adv-accordion\" id=\"eael-adv-accordion-c110539\" data-scroll-on-click=\"no\" data-scroll-speed=\"300\" data-accordion-id=\"c110539\" data-accordion-type=\"accordion\" data-toogle-speed=\"300\">\n            <div class=\"eael-accordion-list\">\n\t\t\t\t\t<div id=\"rfrences\" class=\"elementor-tab-title eael-accordion-header\" tabindex=\"0\" data-tab=\"1\" aria-controls=\"elementor-tab-content-2021\"><span class=\"eael-advanced-accordion-icon-closed\"><\/span><span class=\"eael-advanced-accordion-icon-opened\"><\/span><span class=\"eael-accordion-tab-title\">R\u00e9f\u00e9rences<\/span><i aria-hidden=\"true\" class=\"fa-toggle fas fa-plus\"><\/i><\/div><div id=\"elementor-tab-content-2021\" class=\"eael-accordion-content clearfix\" data-tab=\"1\" aria-labelledby=\"rfrences\"><p><i><span style=\"font-weight: 400\">About Loeys-Dietz Syndrome<\/span><\/i><span style=\"font-weight: 400\">. Loeys-Dietz Syndrome Foundation. (n.d.). Retrieved October 11, 2022, from https:\/\/www.loeysdietz.org\/en\/medical-information#treatment<\/span><\/p><p><span style=\"font-weight: 400\">Caffrey, A. R., &amp; Borrelli, E. P. (2020). The art and science of drug titration. <\/span><i><span style=\"font-weight: 400\">Therapeutic Advances in Drug Safety<\/span><\/i><span style=\"font-weight: 400\">, <\/span><i><span style=\"font-weight: 400\">11<\/span><\/i><span style=\"font-weight: 400\">, 204209862095891. https:\/\/doi.org\/10.1177\/2042098620958910\u00a0<\/span><\/p><p><span style=\"font-weight: 400\">Gouda, P., Kay, R., Habib, M., Aziz, A., Aziza, E., &amp; Welsh, R. (2022). Clinical features and complications of Loeys-Dietz Syndrome: A systematic review. <\/span><i><span style=\"font-weight: 400\">International Journal of Cardiology<\/span><\/i><span style=\"font-weight: 400\">, <\/span><i><span style=\"font-weight: 400\">362<\/span><\/i><span style=\"font-weight: 400\">, 158\u2013167. https:\/\/doi.org\/10.1016\/j.ijcard.2022.05.065\u00a0<\/span><\/p><p><span style=\"font-weight: 400\">Isselbacher E, Preventza O, et al. 2022 ACC\/AHA Guideline for the Diagnosis and Management of Aortic Disease.\u00a0<i>J Am Coll Cardiol.\u00a0<\/i>2022 Dec, 80 (24) e223\u2013e393.<span class=\"citation__editorial-comment\"><a class=\"citation__doi__link\" href=\"https:\/\/doi.org\/10.1016\/j.jacc.2022.08.004\">https:\/\/doi.org\/10.1016\/j.jacc.2022.08.004<\/a><\/span><\/span><\/p><p><span style=\"font-weight: 400\">Loeys, B. L., &amp; Dietz, H. C. (2008, February 28; updated 2018 March 1). Loeys-Dietz Syndrome. <\/span><i><span style=\"font-weight: 400\">GeneReviews<\/span><\/i><span style=\"font-weight: 400\">. Retrieved October 11, 2022, from https:\/\/www.ncbi.nlm.nih.gov\/books\/NBK1133\/.\u00a0<\/span><\/p><p><i><span style=\"font-weight: 400\">Loeys-Dietz Syndrome: Allergies<\/span><\/i><span style=\"font-weight: 400\">. Loeys-Dietz Syndrome Foundation. (n.d.). Retrieved October 11, 2022, from https:\/\/static1.squarespace.com\/static\/5be355670dbda39d591a525e\/t\/6222b1c31c636258a8c1f654\/1646440902459\/LDSF_AllergyRevised_Design+Update+3.4.22.pdf\u00a0<\/span><\/p><p><span style=\"font-weight: 400\">MacCarrick, G., Black, J. H., Bowdin, S., El-Hamamsy, I., Frischmeyer-Guerrerio, P. A., Guerrerio, A. L., Sponseller, P. D., Loeys, B., &amp; Dietz, H. C. (2014). Loeys\u2013Dietz Syndrome: A primer for diagnosis and management. <\/span><i><span style=\"font-weight: 400\">Genetics in Medicine<\/span><\/i><span style=\"font-weight: 400\">, <\/span><i><span style=\"font-weight: 400\">16<\/span><\/i><span style=\"font-weight: 400\">(8), 576\u2013587. https:\/\/doi.org\/10.1038\/gim.2014.11\u00a0<\/span><\/p><p><span style=\"font-weight: 400\">Zaleska. (2022, August 18). <\/span><i><span style=\"font-weight: 400\">Have eczema? How your diet may play a role<\/span><\/i><span style=\"font-weight: 400\">. Cleveland Clinic Health Essentials. Retrieved October 11, 2022, from https:\/\/health.clevelandclinic.org\/eczema-diet\/?utm_source=feedotter&amp;utm_medium=email&amp;utm_campaign=FO-11-03-2021&amp;utm_content=httpshealthclevelandclinicorgeczemadiet&amp;mkt_tok=NDM0LVBTQS02MTIAAAGAi0vfOnlXY-4cUOjP_rE6BQzQyEHHkBTX5l_6VSE7oY6oybjBUu0qKH5dXGZ5zDHQSNxPLoG5TscRb_DukOdQ05K0iC7lSwL1agAl_Wi4eNRjM6E<\/span><\/p><\/div>\n\t\t\t\t\t<\/div><\/div>\t\t\t\t<\/div>\n\t\t\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/div>\n\t\t\t\t\t<\/div>\n\t\t<\/section>\n\t\t\t\t<\/div>\n\t\t","protected":false},"excerpt":{"rendered":"<p>Traitement Philosophies de traitement pour le syndrome de Loeys-Dietz Une approche individualis\u00e9e Le traitement et la prise en charge diff\u00e8rent d\u2019une personne \u00e0 l\u2019autre car le SLD peut affecter les [&hellip;]<\/p>\n","protected":false},"author":1,"featured_media":0,"parent":4444,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"om_disable_all_campaigns":false,"_monsterinsights_skip_tracking":false,"_monsterinsights_sitenote_active":false,"_monsterinsights_sitenote_note":"","_monsterinsights_sitenote_category":0,"site-sidebar-layout":"no-sidebar","site-content-layout":"page-builder","ast-site-content-layout":"default","site-content-style":"default","site-sidebar-style":"default","ast-global-header-display":"","ast-banner-title-visibility":"","ast-main-header-display":"","ast-hfb-above-header-display":"","ast-hfb-below-header-display":"","ast-hfb-mobile-header-display":"","site-post-title":"disabled","ast-breadcrumbs-content":"","ast-featured-img":"disabled","footer-sml-layout":"","ast-disable-related-posts":"","theme-transparent-header-meta":"default","adv-header-id-meta":"","stick-header-meta":"","header-above-stick-meta":"","header-main-stick-meta":"","header-below-stick-meta":"","astra-migrate-meta-layouts":"default","ast-page-background-enabled":"default","ast-page-background-meta":{"desktop":{"background-color":"","background-image":"","background-repeat":"repeat","background-position":"center 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